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Dernières publications
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Julia Pereira Lemos, Liliane Patrícia Gonçalves Tenório, Vincent Mouly, Gillian Butler-Browne, Daniella Arêas Mendes-Da-Cruz, et al.. T cell biology in neuromuscular disorders: a focus on Duchenne Muscular Dystrophy and Amyotrophic Lateral Sclerosis. Frontiers in Immunology, 2023, 14, pp.120283. ⟨10.3389/fimmu.2023.1202834⟩. ⟨hal-04603915⟩
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
Chiffres clés
103
Publications avec texte intégral
Open Access
60 %
Mots clés
Alphavirus
Mass spectrometry
Cross-bridge kinetics
Duchenne muscular dystrophy
Functional genomics
Fibrosis
Metabolism
Arbovirus
2-D PAGE
Akt
Ageing
Haploinsufficiency
DNA methylation
Alzheimer's disease
Myositis
Dystrophie musculaire oculopharyngée
Exon-skipping
Lamins
Anti-acetylcholine receptor antibodies
Myopathies
Atrophy
Satellite cell
ARN
Actin
Myopathy
Aged
Thérapie génique
Triplet expansion disease
Myoblast
DMD
GENE
Accelerometry
Agrégats de PABPN1
Neuromuscular disease
AChR antibodies
Dysferlin
Gene therapy
DUX4
Muscle stem cells
FAPs
Muscle
AUTOPHAGY
Dysferlinopathy
Pharyngeal muscle
Annexin A2
Anti-fibrotic pharmacotherapies
APOPTOSIS
Epigenetics
ALS
Differentiation
Inflammation
Antiserum
BINDING SPECIFICITY
Myotube
Pax7
Bile salt hydrolases
PABPN1 agregates
MUTATIONS
Effector T cells
Human
Biomarker
Skeletal muscle
Regenerative medicine
OPMD
Antisens oligonucleotides
Andermann syndrome
Xenograft
Regulatory T cells
PABPN1
Muscle fibrosis
Regeneration
Cell therapy
Omics
Autologous
RNA
Muscle strength
Transcriptomics
Aggregate
Muscular dystrophy
Adipose tissue
Myoblasts
Calcium
Muscle dystrophy
Geriatric assessment
AAV vectors
Nuclear envelope
Myogenesis
Sarcopenia
Gene replacement
Myosin
Neuromuscular junction NMJ
Aav-U7
Dystrophin
Oculopharyngeal muscular dystrophy
FSHD
Satellite cells
AAV
Intercellular communication
Autoimmune diseases
Amyotrophic Lateral Sclerosis